Tab Application Banner
  • Users Online: 772
  • Home
  • Print this page
  • Email this page
Home About us Editorial board Ahead of print Current issue Search Archives Submit article Instructions Subscribe Contacts Login 
Year : 2016  |  Volume : 11  |  Issue : 4  |  Page : 222-225

Compressive myelopathy: A rare clinical presentation of IgG4-related disease

1 Institute of Rheumatology, Madras Medical College, Chennai; Department of Rheumatology, Saveetha Medical College Hospital, Kanchipuram, Tamil Nadu, India
2 Institute of Rheumatology, Madras Medical College, Chennai, Tamil Nadu, India

Correspondence Address:
Dr. Kavitha Mohanasundaram
6, First Street, Shanthi Nagar, Adambakkam, Chennai - 600 088, Tamil Nadu
Login to access the Email id

Source of Support: None, Conflict of Interest: None

DOI: 10.4103/0973-3698.193587

Rights and Permissions

IgG4-related disease (IgG4RD) is a new entry into the field of rheumatology characterized by tumefactive lesions, storiform fibrosis, and involvement of more than one organ. The most common organ involved is the pancreas which often coexist with mass lesions in other organs. We report a case where IgG4RD presented with the involvement of aorta and meninges in the form of periaortitis and hypertrophic pachymeningitis respectively, a rare coexistence in IgG4RD. The patient responded well to rituximab in the initial visit, however during subsequent recurrence, the response was not significant. We also discuss the immunosuppressants used in IgG4 RD and the variability in clinical response during various stages of disease.

Print this article     Email this article
 Next article
 Previous article
 Table of Contents

 Similar in PUBMED
   Search Pubmed for
   Search in Google Scholar for
 Related articles
 Citation Manager
 Access Statistics
 Reader Comments
 Email Alert *
 Add to My List *
 * Requires registration (Free)

 Article Access Statistics
    PDF Downloaded166    
    Comments [Add]    
    Cited by others 1    

Recommend this journal